Management Team

Multisystem atrophy (MSA)

Overview

Multisystem atrophy is a progressive neurodegenerative disease, which affects the autonomic system and the motor system.

MSA is caused due to deposition of abnormal synuclein protein (synucleinopathy) in the brain.

  • Genetic variations in certain genes including SNCA and LRRK2
  • Age group: 50-60 years
  • Male sex
  • History of neurological conditions such as Parkinson's disease
  • Vascular risk factors including hypertension, diabetes mellitus, hyperlipidaemia,
  • Exposure to solvents, certain types of plastic or metal, and other potential toxins
  • Rapid eye movement (REM) sleep behaviour disorder
  • Autonomic nervous system conditions

  • Autonomic disturbances such as postural hypotension and urinary incontinence
  • Parkinsonian signs such as bradykinesia and rigidity
  • Cerebellar signs such as ataxia and inability to coordinate
  • Pyramidal signs such as weakness and spasticity
  • Myoclonic jerks
  • Sleep disorders such as sleep apnoea, REM behavioural disorders, excessive daytime sleepiness, and nocturnal sleep disturbances
  • Respiratory complications such as stridor
  • Dysphagia at later stages
  • Cognitive disability in later stages

Neurologist

  • Clinical history and examination
  • MRI Brain to determine hot cross bun sign in brain stem.
  • Polysomnography to check for sleep disorders
  • Autonomic nervous testing

  • No specific treatment is available.
  • Supportive care for prevention of orthostatic hypotension, sleep disorders, dysphagia, stridor, and parkinsonian symptoms
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